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- 详细信息
- 文献和实验
- 技术资料
- 供应商:
南京赛泓瑞
- 检测范围:
46.88-3000pg/mL The standard curve concentrations used for the ELISA’s were 3000pg/mL, 1500pg/mL, 750pg/mL, 375pg/mL, 187.5pg/mL, 93.75pg/mL, 46.88pg/mL
- 检测方法:
elisa
- 应用:
elisa
- 适应物种:
Rattus norvegicus (Rat)
- 样本:
Plasma
- 规格:
48T/96T
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文献和实验Multimeric Analysis of von Willebrand Factor
immunoelectrophoresis (2D-IEP). In 1974, Kernoff et al. (2 ) used this method, and since then multimer sizing of von Willebrand Factor Antigen (vWF∶Ag) in this form and other variations have been used in the diagnosis and classification of von Willebrand’s disease (vWD).
Screening for Candidate Mutations Causing von Willebrands Disease (vWD)
von Willebrand factor (vWF) is a large, complex glycoprotein that exists in plasma and platelets, and is synthesized by megakaryocytes and endothelial cells. vWF plays an essential role in hemostasis in at least two ways. It is involved
,是 FVIII 存在的基础。通过特殊的方法从血浆中联合提存的这两种蛋白,利用化学计算法,可知血浆中 FVIII 与 VWF 约为 1 : 50 , VWF 占 FVIII—VWF 复合物的 98% ,可见, VWF 过量于 FVIII 。所以, FVIII 升高并非是 VWF 升高所致。 [1 , 2 , 3] 非 O 型血组比 O 型血组患血栓的危险性要增高。 VWF 是 FVIII 的载体、保护蛋白,血友病患者由于 FVIII 缺乏,但 VWF 正常,血小板功能正常,发生
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