Store at -20°C. Supplied in 50nM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.
适应物种:
Human, Mouse, Rat
保质期:
12个月
库存:
现货
宿主:
Rabbit
应用范围:
WB,IHC,ICC/IF,FC
靶点:
NAGLU
规格:
20μL/50μL/100μL
规格:
20μL
产品价格:
¥600.0
规格:
50μL
产品价格:
¥1000.0
规格:
100μL
产品价格:
¥1800.0
This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate. [provided by RefSeq, Jul 2008]