原纤维蛋白1抗体

原纤维蛋白1抗体产品类别

兔抗人、大、小鼠FBN1抗体

产品价格

0.1ml/480元 0.2ml/650元

产品标准

浓缩液(1mg/1ml) 亲和纯化抗体

产品应用

WB=1:100-500 Elisa =1:200-1000 IP=1:20-100 IHC=1:100-500 （石蜡切片需做抗原修复）

原纤维蛋白1抗体产品介绍

Fibrillin-1广泛存在于皮肤、肺、肾、血管、软骨、睫装小体等，原纤维蛋白1在产生强而韧性的组织中起重要作用，是组织连结重要的蛋白。
Fibrillin is the major constitutive element of extracellular microfibrils and has widespread distribution in both elastic and nonelastic connective tissue throughout the body. The cDNA was identified in 1991 and was mapped coincident with the locus for Marfan syndrome. Subsequent studies confirmed that mutations in the Fibrillin 1 gene are the major cause of Marfan syndrome. The connective tissue protein has a widespread distribution in the connective tissue matrices of skin, lung, kidney, vasculature, cartilage, tendon, muscle, cornea, and ciliary zonule.
mol wt:Fibrillin 1 is an extracellular acidic protein with a high cysteine content and an extended threadlike shape with mosaic composition of different types of extracellular modules. Most of the fibrillin molecule is contributed by 47 epidermal growth factor like (EGF like) repeats; 43 of them have a consensus sequence for calcium binding (cb). Other modules including 8 cysteine motifs (seven), hybrid motifs (two), and unique domains (three) are interspersed throughout the molecule. Fibrillin 1 contains a proline rich region close to the N terminus that is replaced by a glycine rich region in Fibrillin 2. The fibrillins are found throughout the connective tissue as integral components of extended fibrils.zk-13716R Cadherin 20钙粘蛋白20抗体
zk-13917R CDH29钙粘蛋白29抗体
zk-7351R CD200RCD200受体抗体
zk-13718R Cadherin 26钙粘蛋白26抗体
zk-13721R CDHF14钙粘蛋白14抗体
zk-13706R CLCA3钙激活氯离子通道蛋白3抗体
zk-10521R CD200RCD200受体抗体
zk-13828R CELA1弹性蛋白酶1抗体
zk-7353R c-Kit干细胞生长因子受体/细胞表面分化抗原抗体
zk-13742R CD99L2CD99样蛋白2抗体
zk-13743R CTNNA3钙粘蛋白相关蛋白CTNNA3抗体
zk-13753R Claudin 15紧密连接蛋白15抗体
zk-13754R Claudin 12紧密连接蛋白12抗体
zk-13901R CHIC2CHIC2蛋白抗体
zk-13906R phospho-CHEK1 (Ser286)磷酸化细胞周期检测点激酶1抗体
zk-13907R Phospho-CHK2 (Ser28)磷酸化细胞周期检测点激酶2抗体
zk-13908R Phospho-CHK2 (Ser33 + Ser35)磷酸化细胞周期检测点激酶2抗体
zk-13909R Phospho-CHK2 (Thr26)磷酸化细胞周期检测点激酶2抗体
zk-13910R Phospho-CHK2 (Thr383)磷酸化细胞周期检测点激酶2抗体
zk-13911R CHM遗传性脉络膜缺乏症相关蛋白抗体
zk-13912R CHML遗传性脉络膜缺乏症相关蛋白样抗体
zk-13913R CHMP2A乳腺腺癌标志物CHMP2A抗体
zk-13915R CHMP6染色质修饰蛋白CHMP6抗体
zk-13914R CHMP5染色质修饰蛋白CHMP5抗体
zk-13734R Connexin 31.1间隙连接蛋白31.1抗体
zk-13739R Claudin 10紧密连接蛋白10抗体
zk-13746R Claudin 23紧密连接蛋白23抗体
zk-13747R Claudin 22紧密连接蛋白22抗体
zk-13749R Claudin 19紧密连接蛋白19抗体
原纤维蛋白1抗体