- ￥880
- Bioss
- bs-11714P
- 2025年10月16日
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500ug
| 产品编号 | bs-11714P |
| 英文名称 | CLN5 Antibody Blocking Peptide |
| 中文名称 | 神经细胞蜡样质脂褐质沉积病蛋白CLN5封闭多肽 |
| 英文别名 | Ceroid lipofuscinosis neuronal 5; Ceroid-lipofuscinosis neuronal protein 5; CLN5; CLN5_HUMAN; NCL; Protein CLN5. |
| 纯化方法 | HPLC |
| 研究领域 | Neuroscience > Neurology process > Neurodegenerative disease |
| 亚细胞定位 | Lysosome. |
| 组织特异性 | Ubiquitous. |
| 翻译后修饰 | Glycosylated. |
| 相似性 | Belongs to the CLN5 family. |
| 保存条件 | Shipped at 4℃. Stored at -20℃ for one year. Avoid repeated freeze/thaw cycles. |
| 注意事项 | This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
| 背景资料 | Neuronal ceroid-lipofuscinose (NCL), also designated Batten disease, comprises a group of recessively inherited, progressive neurodegenerative diseases found in children. NCL is characterized by atrophy of the brain and an accumulation of lysosome derived fluorescent bodies found in many cells, especially neurons. Symptoms of NCL include a failure of psychomotor development, seizures, impaired vision and premature death. The eight genes/proteins associated with NCL are designated CLN1-CLN8. Mutations in six of these genes results in a distinct type of NCL-disease; the six genes/proteins are CLN1 (encoding PPT1, a protein thiolesterase), CLN2 (encodeing the serine protease TPP1), CLN3, CLN5, CLN6 and CLN8. A single base duplication mutation in dog and cow CLN5 has been shown to cause NCL. |
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CLN5 Antibody Blocking Peptide(bs-11714P)-500ug
￥880
