- ￥880
- Bioss
- bs-8702P
- 2025年10月16日
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500ug
| 产品编号 | bs-8702P |
| 英文名称 | SLC19A3 Antibody Blocking Peptide |
| 中文名称 | 溶质载体家族19成员3封闭多肽 |
| 英文别名 | Solute carrier family 19 member 3; Thiamine transporter 2; thTr 2; THTR2. |
| 纯化方法 | HPLC |
| 研究领域 | Metabolism > Pathways and Processes > Cofactors, Vitamins / minerals > Vitamins / minerals Signal Transduction > Metabolism > Vitamins / Minerals |
| 亚细胞定位 | Plasma membrane. |
| 组织特异性 | Widely expressed but most abundant in placenta, kidney and liver. |
| 相似性 | Belongs to the reduced folate carrier (RFC) transporter (TC 2.A.48) family. |
| 功能 | Mediates high affinity thiamine uptake, propably via a proton anti-port mechanism. Has no folate transport activity. |
| 保存条件 | Shipped at 4℃. Stored at -20℃ for one year. Avoid repeated freeze/thaw cycles. |
| 注意事项 | This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
| 背景资料 | This gene encodes a ubiquitously expressed transmembrane thiamine transporter that lacks folate transport activity. Mutations in this gene cause biotin-responsive basal ganglia disease (BBGD); a recessive disorder manifested in childhood that progresses to chronic encephalopathy, dystonia, quadriparesis, and death if untreated. Patients with BBGD have bilateral necrosis in the head of the caudate nucleus and in the putamen. Administration of high doses of biotin in the early progression of the disorder eliminates pathological symptoms while delayed treatment results in residual paraparesis, mild mental retardation, or dystonia. Administration of thiamine is ineffective in the treatment of this disorder. Experiments have failed to show that this protein can transport biotin. Mutations in this gene also cause a Wernicke's-like encephalopathy.[provided by RefSeq, Jan 2010] |
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SLC19A3 Antibody Blocking Peptide(bs-8702P)-500ug
￥880
