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- ProSci
- 美国
- PSI-15-377-50uL
- 2025年07月14日
- WB,IHC,IF
- 兔
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- 详细信息
- 文献和实验
- 技术资料
- 免疫原：
Recombinant fusion protein containing a sequence corresponding to amino acids 346-635 of human DMD (NP_004007.1).
- 保存条件：
Store at -20℃
- 保质期：
1年
- 级别：
科研级别
- 库存：
100
- 供应商：
艾美捷科技
- 宿主：
兔
- 应用范围：
WB,IHC,IF
- 抗体英文名：
DMD Antibody
- 抗体名：
DMD Antibody
- 规格：
50uL
DMD 抗体，DMD Antibody，DMD 抗体,DMD Antibody
产品名称：DMD 抗体-DMD Antibody
产品货号：PSI-15-377-50uL
产品规格：50uL
背景资料：This gene spans a genomic range of greater than 2 Mb and encodes a large protein containing an N-terminal actin-binding domain and multiple spectrin repeats. The encoded protein forms a component of the dystrophin-glycoprotein complex (DGC), which bridges the inner cytoskeleton and the extracellular matrix. Deletions, duplications, and point mutations at this gene locus may cause Duchenne muscular dystrophy (DMD), Becker muscular dystrophy (BMD), or cardiomyopathy. Alternative promoter usage and alternative splicing result in numerous distinct transcript variants and protein isoforms for this gene.
保存建议：DMD 抗体-DMD AntibodyStore at -20℃
应用类型：WB,IHC,IF
点击：DMD 抗体-DMD Antibody查看更详细产品说明，更多应用、储存、价格、货期等信息请垂询艾美捷科技有限公司。更多ProSci公司特色试剂盒、特色抗体以及特色试剂等产品评论，请点击查看艾美捷特色产品中心。
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文献和实验杜氏进行性肌营养不良（Duchenne muscular dystrophy，DMD）和贝氏进行性肌营养不良（Becker muscular dystrophy，BMD）系X连锁隐性遗传病，是由于抗肌萎缩蛋白（dystrophin）基因突变所致的肌源性损伤。基因突变的主要类型是基因片段缺失，在基因5‘端和3’端分别存在一个缺失高发区，尤其后者，以外显子51区域为高峰医学|教育网整理搜集，中国人病例近80 %的缺失突变发生在此区域。其中大范围（一个或数个外显子） 缺失型占60 % ，重复型
Systemic Delivery of Antisense Oligomer in Animal Models and Its Implications for Treating DMD
Antisense oligomer (AO)-mediated splicing modulation for treating DMD demands a systemic administration of AOs as pharmacological drugs to achieve effective prevention of disease progression and to improve quality and longevity of patient
Duchenne muscular dystrophy (DMD) is an X-linked recessive neuromuscular disorder caused by mutations in the dystrophin gene at Xp21. Approximately two-thirds of the mutations are intragenic deletions of one or more of the 79 exons
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