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- 详细信息
- 技术资料
- 靶点:
DES
- 应用范围:
IHC 1:200
- 宿主:
Mouse
- 适应物种:
Human, Mouse, Rat
- 保质期:
1-2年
- 供应商:
安诺伦(北京)生物科技有限公司
- 标记物:
Unconjugated
- 克隆性:
Monoclonal Antibody
- 保存条件:
Stable for 1 year at -20°C from date of shipment. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.
- 形态:
Lyophilized powder (original buffer 1X PBS, pH 7.3, 8% trehalose)
- 亚型:
IgG1
- 免疫原:
Full length human recombiant protein of human DES(NP_001918) produced in E.coli.
- 规格:
100 ug
别名:CSM1; CSM2; LGMD2R
产品概述:Carrier-free (BSA/glycerol-free) Desmin mouse monoclonal antibody,clone UMLBI166
总结:This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies. [provided by RefSeq, Jul 2008]
产品概述:Carrier-free (BSA/glycerol-free) Desmin mouse monoclonal antibody,clone UMLBI166
总结:This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies. [provided by RefSeq, Jul 2008]
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Desmin (DES) Mouse Monoclonal Antibody [Clone ID: UMLBI166]
¥3870


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