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- 详细信息
- 技术资料
- 靶点:
GBA
- 应用范围:
WB 1:2000, IHC 1:100
- 宿主:
Mouse
- 适应物种:
Human, Mouse, Rat
- 保质期:
1-2年
- 供应商:
安诺伦(北京)生物科技有限公司
- 标记物:
Unconjugated
- 克隆性:
Monoclonal Antibody
- 保存条件:
Stable for 1 year at -20°C from date of shipment. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.
- 形态:
Lyophilized powder (original buffer 1X PBS, pH 7.3, 8% trehalose)
- 亚型:
IgG1
- 免疫原:
Human recombinant protein fragment corresponding to amino acids 40-315 of human GBA (NP_000148) produced in E.coli.
- 规格:
100 ug
别名:GBA1; GCB; GLUC
产品概述:Carrier-free (BSA/glycerol-free) GBA mouse monoclonal antibody, clone LBI2C12
总结:This gene encodes a lysosomal membrane protein that cleaves the beta-glucosidic linkage of glycosylceramide, an intermediate in glycolipid metabolism. Mutations in this gene cause Gaucher disease, a lysosomal storage disease characterized by an accumulation of glucocerebrosides. A related pseudogene is approximately 12 kb downstream of this gene on chromosome 1. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2010]
产品概述:Carrier-free (BSA/glycerol-free) GBA mouse monoclonal antibody, clone LBI2C12
总结:This gene encodes a lysosomal membrane protein that cleaves the beta-glucosidic linkage of glycosylceramide, an intermediate in glycolipid metabolism. Mutations in this gene cause Gaucher disease, a lysosomal storage disease characterized by an accumulation of glucocerebrosides. A related pseudogene is approximately 12 kb downstream of this gene on chromosome 1. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2010]
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GBA Mouse Monoclonal Antibody [Clone ID: LBI2C12]
¥3300


![GBA Mouse Monoclonal Antibody [Clone ID: LBI2C12]](https://img1.dxycdn.com/2022/0707/344/1496323853485278553-14.jpg)

