N-Iso Valerylglycine

1) Cat. No.: TRC-I917600; 2) Chemical Name: N-Iso Valerylglycine ; 3) CAS No.: 16284-60-9; 4) Mol. Formula: C7H13NO3; 5) Mol. Weight: 159.18; 6) Packing Size: 2.5g / 25g; 7) Appearence: White Solid; 8) Application Notes: N-Isovalerylglycine is a useful diagnostic tool in the diagnosis of many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isovalerylglycine is found in the urine of patients with isovaleric acidemia, an inborn error of leucine metabolism.; 9) Synonym: N-(3-Methyl-1-oxobutyl)glycine; N-Isovalerylglycine; Isovalerylglycine; N-Isovaleroylglycine;; 10) Solubility: DMSO, Methanol; 11) Storage condition: Refrigerator; 12) References: Tanaka, K. et al.: J. Biol. Chem., 242, 2966 (1967); Bonafe, L. et al.: Mol. Gen. Metab., 69, 311 (2000);