产品封面图

GCSH Antibody Blocking Peptide

(bs-13323P)-500ug
收藏
  • ¥880
  • Bioss已认证
  • bs-13323P
  • 2025年10月16日
    avatar
    品牌商
    10钻石会员
  • 企业认证

    点击 QQ 联系

    • 详细信息
    • 文献和实验
    • 技术资料
    • 规格

      500ug

    产品编号bs-13323P
    英文名称GCSH Antibody Blocking Peptide
    中文名称甘氨酸裂解系统H蛋白封闭多肽
    英文别名GCE; GCSH; GCSH_HUMAN; Glycine cleavage system H protein; Glycine cleavage system H protein mitochondrial; Glycine cleavage system protein H (aminomethyl carrier); Glycine cleavage system protein H; Lipoic acid containing protein; mitochondrial; Mitochondrial glycine cleavage system H protein; NKH.
    纯化方法HPLC
    亚细胞定位Mitochondrion.
    相似性Belongs to the gcvH family.
    Contains 1 lipoyl-binding domain.
    功能The glycine cleavage system catalyzes the degradation of glycine. The H protein shuttles the methylamine group of glycine from the P protein to the T protein.
    保存条件Shipped at 4℃. Stored at -20℃ for one year. Avoid repeated freeze/thaw cycles.
    注意事项This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
    背景资料GCSH is a 173 amino acid mitochondrial protein that contains one lipoyl-binding domain and belongs to the gcvH family. Defects in the gene encoding GCSH are the cause of glycine encephalopathy (GCE), an autosomal recessive disease that is also referred to as non-ketotic hyperglycinemia (NKH). Characterized by severe neurological symptoms, patients with GCE have a large amount of glycine accumulated in their body fluids. The gene encoding GCSH maps to human chromosome 16, which encodes over 900 genes and comprises nearly 3% of the human genome.

     

     

    风险提示:丁香通仅作为第三方平台,为商家信息发布提供平台空间。用户咨询产品时请注意保护个人信息及财产安全,合理判断,谨慎选购商品,商家和用户对交易行为负责。对于医疗器械类产品,请先查证核实企业经营资质和医疗器械产品注册证情况。

    图标文献和实验
    相关实验
    图标技术资料

    暂无技术资料 索取技术资料

    同类产品报价

    产品名称
    产品价格
    公司名称
    报价日期
    ¥1680
    武汉博欧特生物科技有限公司
    2025年07月12日询价
    ¥880
    北京博奥森生物技术有限公司
    2025年10月16日询价
    ¥700
    上海淳麦生物科技有限公司
    2025年08月13日询价
    ¥700
    安元生物科技(南京)有限公司
    2025年05月04日询价
    ¥1680
    武汉琼格生物科技有限公司
    2026年01月29日询价
    GCSH Antibody Blocking Peptide(bs-13323P)-500ug
    ¥880