- ￥2980
- Bioss
- bs-13254R-Cy5
- 2025年09月30日
- 产品信息以Bioss网站为准
企业认证
相关产品推荐更多 >
phospho-c-Kit (Tyr730) Rabbit pAb, PerCP-Cy7 conjugated(bs-12914R-PerCP-Cy7)-100ul
￥2980ORC3 Rabbit pAb, Biotin conjugated(bs-18023R-Bio)-100ul
￥2980Osteocalcin Rabbit pAb, Biotin conjugated(bs-0470R-Bio)-100ul
￥2980
NLGN2 Rabbit pAb(bs-11098R)-50ul/100ul/200ul
￥1180PTF1A Rabbit pAb, HRP conjugated(bs-22058R-HRP)-100ul
￥2980
万千商家帮你免费找货
0 人在求购买到急需产品
- 详细信息
- 技术资料
- 应用范围：
产品信息以Bioss网站为准
- 规格：
100ul
| 产品编号 | bs-13254R-Cy5 |
| 英文名称 | GAA Rabbit pAb, Cy5 conjugated |
| 中文名称 | Cy5标记的α葡萄糖苷酶/溶酶体α-葡糖苷酶抗体 |
| 英文别名 | 70 kDa lysosomal alpha-glucosidase; Acid alpha glucosidase; Acid maltase; Aglucosidase alfa; alpha glucosidase; GAA; Glucosidase alpha acid(Pompe disease glycogen storage disease type II); Glucosidase alpha acid; Glucosidase alpha; LYAG; LYAG_HUMAN; Lysosomal alpha glucosidase. |
| 产品应用 | IF=1:200-800 Not yet tested in other applications. |
| 抗体来源 | Rabbit |
| 免疫原 | KLH conjugated synthetic peptide derived from human GAA/Glucosidase alpha |
| 亚型 | IgG |
| 纯化方法 | affinity purified by Protein A |
| 克隆类型 | Polyclonal |
| 浓度 | 1mg/ml |
| 储存液 | 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol. |
| 研究领域 | Metabolism > Pathways and Processes > Metabolic signaling pathways > Energy transfer pathways > Energy Metabolism Signal Transduction > Metabolism > Energy Metabolism |
| 亚细胞定位 | Lysosome. Lysosome membrane. |
| 翻译后修饰 | The different forms of acid glucosidase are obtained by proteolytic processing. _x000D_ Phosphorylation of mannose residues ensures efficient transport of the enzyme to the lysosomes via the mannose 6-phosphate receptor. |
| 相似性 | Belongs to the glycosyl hydrolase 31 family. _x000D_ Contains 1 P-type (trefoil) domain. |
| 功能 | Essential for the degradation of glygogen to glucose in lysosomes._x000D_ Subcellular Location : Lysosome. Lysosome membrane. |
| 保存条件 | Shipped at 4℃. Store at -20°C for one year. Avoid repeated freeze/thaw cycles. |
| 注意事项 | This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
| 背景资料 | This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Jul 2008]. |
| 应用 | 推荐稀释比例 |
| {IF} | {1:200-800} |
风险提示：丁香通仅作为第三方平台，为商家信息发布提供平台空间。用户咨询产品时请注意保护个人信息及财产安全，合理判断，谨慎选购商品，商家和用户对交易行为负责。对于医疗器械类产品，请先查证核实企业经营资质和医疗器械产品注册证情况。
技术资料暂无技术资料 索取技术资料
GAA Rabbit pAb, Cy5 conjugated(bs-13254R-Cy5)-100ul
￥2980
