IKBKG 抗体-IKBKG Antibody

IKBKG 抗体，IKBKG Antibody，IKBKG 抗体,IKBKG Antibody

产品名称：IKBKG 抗体-IKBKG Antibody

产品货号：PSI-27-263-100ul

产品规格：100ul

背景资料：Familial incontinentia pigmenti (IP) is a genodermatosis that segregates as an X-linked dominant disorder and is usually lethal prenatally in males . In affected females it causes highly variable abnormalities of the skin, hair, nails, teeth, eyes, and central nervous system. The prominent skin signs occur in 4 classic cutaneous stages: perinatal inflammatory vesicles, verrucous patches, a distinctive pattern of hyperpigmentation, and dermal scarring. Cells expressing the mutated X chromosome are eliminated selectively around the time of birth, so females with IP exhibit extremely skewed X-inactivation. Familial incontinentia pigmenti is caused by mutations in the NEMO gene and is here referred to as IP2, or 'classical' incontinentia pigmenti. Sporadic incontinentia pigmenti, the so-called IP1, which maps to Xp11, is categorized as hypomelanosis of Ito

保存建议：IKBKG 抗体-IKBKG AntibodyFor short periods of storage (days) store at 4℃

应用类型：E, WB

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