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- 详细信息
- 文献和实验
- 技术资料
- 靶点:
IDS
- 浓度:
0.79 mg/ml
- 应用范围:
WB 1:2000, IHC 1:150, IF 1:100, FLOW 1:100
- 宿主:
Mouse
- 适应物种:
Human, Mouse
- 保质期:
1-2年
- 供应商:
安诺伦(北京)生物科技有限公司
- 标记物:
Unconjugated
- 克隆性:
Monoclonal Antibody
- 保存条件:
Store at +4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.
- 形态:
PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
- 亚型:
IgG2a
- 免疫原:
Full length human recombinant protein of human IDS(NP_000193) produced in HEK293T cell.
- 规格:
100 ul/30 ul
| 规格: | 100 ul | 产品价格: | ¥2025.0 |
|---|---|---|---|
| 规格: | 30 ul | 产品价格: | ¥690.0 |
产品概述:IDS (Iduronate 2 sulfatase) mouse monoclonal antibody, clone LBI3B10
总结:Iduronate-2-sulfatase is required for the lysosomal degradation of heparan sulfate and dermatan sulfate. Mutations in this X-chromosome gene that result in enzymatic deficiency lead to the sex-linked Mucopolysaccharidosis Type II, also known as Hunter Syndrome. Iduronate-2-sulfatase has a strong sequence similarity with human arylsulfatases A, B, and C, and human glucosamine-6-sulfatase. Multiple alternatively spliced transcript variants that encode different protein isoforms have been described. [provided by RefSeq]
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文献和实验it is recommended to stain the nuclear membrane in both embryos and discs with a monoclonal antibody specific for Drosophila lamin and a secondary goat anti-mouse Cy5 labelled secondary antibody (see alternative protocol). Alternative method for fixation
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