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Pyruvate Dehydrogenase E1 beta

subunit
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  • ¥1125 - 1875
  • HuaBio/华安生物
  • ET1705-57
  • 2025年07月07日
  • WB, IHC-P, IP, FC
  • Rabbit
  • Human, Mouse, Rat
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    • 详细信息
    • 文献和实验
    • 技术资料
    • 免疫原

      Synthetic peptide within Human Pyruvate Dehydrogenase E1 beta subunit aa 310-359 / 359.

    • 亚型

      IgG

    • 形态

      Liquid

    • 克隆性

      Recombinant Rabbit monoclonal Antibody

    • 标记物

      Non-conjugated

    • 适应物种

      Human, Mouse, Rat

    • 库存

      现货

    • 供应商

      华安生物

    • 宿主

      Rabbit

    • 应用范围

      WB, IHC-P, IP, FC

    • 浓度

      1 mg/mL.

    • 规格

      50ul/100ul

    规格:50ul产品价格:¥1125.0
    规格:100ul产品价格:¥1875.0
    The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO. It contains multiple copies of three enzymatic components: pyruvate dehydrogenase (E1), dihydrolipoamide acetyltransferase (E2) and lipoamide dehydrogenase (E3). Defects in PDHB are a cause of pyruvate dehydrogenase E1 component deficiency (PDHE1 deficiency). PDHE1 deficiency is the most common enzyme defect in patients with primary lactic acidosis. It is associated with variable clinical phenotypes ranging from neonatal death to prolonged survival complicated by developmental delay, seizures, ataxia, apnea, and in some cases to an X-linked form of Leigh syndrome (LS) (Leigh encephalomyelopathy).

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    图标文献和实验
    相关实验
    • [资源] 所有的看家基因(housekeeping genes)列表+引物设计服务

      protein), beta 1, 88kDa (CTNNB1), mRNA 1165 NM_003753 Homo sapiens eukaryotic translation initiation factor 3, subunit 7 zeta, 66/67kDa (EIF3S7), mRNA 1363 NM_004541 Homo sapiens NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa (NDUFA1

    • 45种常见蛋白质分子量参考

      化酶a[phosphorylase a] 血清白蛋白[serum albumin] L-氨基酸氧化酶[L-amino acid oxidase] 地氧化氢酶[catalase] 丙酮酸激活酶[pyruvate kinase] 谷氨酸脱氢酶[glutamate dehydrogenase] 亮氨酸氨肽酶[glutamae dehydrogenase] γ-球蛋白,H链[γ-globulin, H chain]

    • 线粒体荧光探针大全:TMRM,Mitotracker,JC-1

      marker for immunohistochemistry.117 Monoclonal antibodies against both human and yeast porin are available from Molecular Probes (A21317, A31855, A6449; Table 12.6). Pyruvate Dehydrogenase Molecular Probes has available a series of antibodies

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    Pyruvate Dehydrogenase E1 beta subunit
    ¥1125 - 1875